Resumen. DIAZ CONCEPCION, Alina. Acquired von Willebrand’s disease. General aspects. Rev Cubana Hematol Inmunol Hemoter [online]. , vol, n La hemofilia A adquirida (HAA) es un trastorno hemorrágico poco frecuente entre otros, enfermedades autoinmunes y malignas y durante el embarazo, parto y .. of the management of acquired haemophilia and von Willebrand syndrome. enfermedad von willebrand adquirida pdf. Quote. Postby Just» Tue Aug 28, am. Looking for enfermedad von willebrand adquirida pdf. Will be.
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Ciudad de La Habana, Cuba. Con la azatiopina, la ciclosporina, la vincristina y el micofenolato de mofetil, se han obtenido resultados variables.
Approximately in half of cases it is noted a heterogeneous group of pathological processes including among others, autoimmune and malignant diseases and during pregnancy, labor and puerperium. Hemorrhagic manifestations are variable and mainly of mucous cutaneous type.
AHA treatment includes the control of hemorrhagic manifestations and the suppression of antibody production. As alternative therapy in some cases the FCIII concentration, the plasmapheresis and extracorporeal immuno-adsorption may be used. The prednisone alone or associated with cyclophosphamide is the firs-line immunosuppressive treatment.
In refractory patients it may be administered as a second-line therapy, the Rituximab anti-CD With the use of Azathioprine, Cyclosporine, Vincristine and the Mycophenolate mofetil variable results have been achieved. Los productos que sortean el efecto del inhibidor: Con el uso de otros inmunosupresores como terapia alternativa se han obtenido respuestas variables.
Los resultados del tratamiento con IgG endovenosa en altas dosis en pacientes con HAA, han sido en general pobres. Acquired hemophilia A in the United Kingdom. A population based unselected, consecutive cohort of patients with acquired haemophilia A. Br J Haematol ; The management of acquired haemophilia. Haemophilia ;12 Suppl 5: A survey of patients with acquired hemophilia in a hemophilia centre over year-period. Clin Lab Haematol ; Baillieres Clin Haematol ;9: A more uniform measurement of factor VIII inihibitors.
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What is the abbreviation for enfermedad de von Willebrand adquirida?
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A review adquidida the literature with special reference to the value of steroid and immunosuppresive treatment. Baudo F, de Cataldo F. Br J Obstet Gynecol ; Postpartum acquired factor VIII inhibitors: Results of a survey. Am J Hematol ; Bona S, Hantoushzadeh S. Acquired hemophilia as a cause of primary post-partum hemorrhage. Acta Iran Med ; Postpartum acquired haemophilia clinical recognition and management.
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Successful use of recombinant factor VIIa in a patient with severe hemophilia A during synovectomy. Rev Cub Hematol Inmunol Hemoter ;26 2. The use of recombinant factor VIIa in the treatment of bleeding disorders. Treatment of acquired haemophilia with recombinant activated FVII: The treatment of bleeding in acquired haemophilia with recombinant factor VIIa: Abshire T, Kenet G.
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EVWA – enfermedad de von Willebrand adquirida
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