Resumen. DIAZ CONCEPCION, Alina. Acquired von Willebrand’s disease. General aspects. Rev Cubana Hematol Inmunol Hemoter [online]. , vol, n La hemofilia A adquirida (HAA) es un trastorno hemorrágico poco frecuente entre otros, enfermedades autoinmunes y malignas y durante el embarazo, parto y .. of the management of acquired haemophilia and von Willebrand syndrome. enfermedad von willebrand adquirida pdf. Quote. Postby Just» Tue Aug 28, am. Looking for enfermedad von willebrand adquirida pdf. Will be.

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Ciudad de La Habana, Cuba. Con la azatiopina, la ciclosporina, la vincristina y el micofenolato de mofetil, se han obtenido resultados variables.

Approximately in half of cases it is noted a heterogeneous group of pathological processes including among others, autoimmune and malignant diseases and during pregnancy, labor and puerperium. Hemorrhagic manifestations are variable and mainly of mucous cutaneous type.


AHA treatment includes the control of hemorrhagic manifestations and the suppression of antibody production. As alternative therapy in some cases the FCIII concentration, the plasmapheresis and extracorporeal immuno-adsorption may be used. The prednisone alone or associated with cyclophosphamide is the firs-line immunosuppressive treatment.

In refractory patients it may be administered as a second-line therapy, the Rituximab anti-CD With the use of Azathioprine, Cyclosporine, Vincristine and the Mycophenolate mofetil variable results have been achieved. Los productos que sortean el efecto del inhibidor: Con el uso de otros inmunosupresores como terapia alternativa se han obtenido respuestas variables.

Los resultados del tratamiento con IgG endovenosa en altas dosis en pacientes con HAA, han sido en general pobres. Acquired hemophilia A in the United Kingdom. A population based unselected, consecutive cohort of patients with acquired haemophilia A. Br J Haematol ; The management of acquired haemophilia. Haemophilia ;12 Suppl 5: A survey of patients with acquired hemophilia in a hemophilia centre over year-period. Clin Lab Haematol ; Baillieres Clin Haematol ;9: A more uniform measurement of factor VIII inihibitors.


Thromb Diath Haemorr ; Acquired inhibitors in non-hemophilic patients. Am J Haematol ; Experience of two Italian Centres with 17 new cases. Acquired inhibitors in malignant and non malignant disease state. Am J Med ; Acquired disorders of coagulation. Basic Principles and Clinical Practice. Lippincott, Williams and Wilkins; Acquired hemophilia in patients with hematologic malignancies.

What is the abbreviation for enfermedad de von Willebrand adquirida?

Arch Pathol Lab Med ; Sallah S, Wan JY. Inhibitors against factor VIII in patients with cancer.

Analysis of 41 patients. Review and meta-analysis focused on therapy and prognostic factors. Acquired hemophilia in women post partum: Clinical manifestations, diagnosis and treatment. Clin Appl Thromb Hemost ;6: Santoro RC, Prejano S. Postpartum acquired hemophilia A: A description of three cases and literature review. Blood Coagulat Fibrinolysis ; Post partum factor VIII inihibitors.

A review adquidida the literature with special reference to the value of steroid and immunosuppresive treatment. Baudo F, de Cataldo F. Br J Obstet Gynecol ; Postpartum acquired factor VIII inhibitors: Results of a survey. Am J Hematol ; Bona S, Hantoushzadeh S. Acquired hemophilia as a cause of primary post-partum hemorrhage. Acta Iran Med ; Postpartum acquired haemophilia clinical recognition and management.

Epidemiology and general guidelines of the management of acquired haemophilia and von Willebrand syndrome. Acquired hemophilia first manifesting as life-threatening intracranial vom Case Report Neurol Med Chir ; Detection of factor VIII inhibitors with the partial thromboplastin time.

Laboratory tests for factor VIII inhibitors their variation, significance and interpretation. Blood Coagul Fibrinolysis ;2 Suppl 1: Deep venous thrombosis and lupus anticoagulant. Inactivation of factor VIII coagulant activity by two different types of human antibodies. Guidelines on the investigation and management of the anti-phospholipid adquirjda. International recommendations on the diagnosis and treatment of patients with acquired hemophilia A. Treatment of acquired haemophilia with factor eight inhibitor bypassing activity.


Successful use of recombinant factor VIIa in a patient with severe hemophilia A during synovectomy. Rev Cub Hematol Inmunol Hemoter ;26 2. The use of recombinant factor VIIa in the treatment of bleeding disorders. Treatment of acquired haemophilia with recombinant activated FVII: The treatment of bleeding in acquired haemophilia with recombinant factor VIIa: Abshire T, Kenet G.

J Thromb Haemost ;2: Acquired hemophilia; A critical bleeding syndrome. Br Med J ; Management of severe hemorrhage and inhibitor elimination in acquired hemophilia. The modified Heidelberg-Malmo protocol.

Extracorporeal immunoadsorption for the treatment of coagulation inhibitors. Semin Thromb Hemost ; Mudad R, Kane WH. Case report and review of the literature.

Cytotoxic suppression of acquired factor VIII: A prospective, randomized trial of prednisone and cyclophosphamide in the treatment of patients with factor VIII autoantibodies. Acquired hemophilia A with sigmoid colon cancer: Successful treatment with Rituximab followed by sigmoidectomy.

EVWA – enfermedad de von Willebrand adquirida

Int J Hematol ; A rapidly progressive life-threatening postpartum hemorrhage: Successful treatment with anti-CD20 monoclonal antibody.

Rituximab for autoimmune haemophilia: A proposed treatment algorithm. Rituximab in the treatment of adult acquired hemophilia A: Crit Rev Oncol Hematol ; Chop chemotherapy plus Rituximab compared with chop alone in elderly patients with diffuse large-B-cell lymphoma.

N Engl J Med ; Tolerability and safety of Rituximab Mabthera. Cancer Treat Rev ; Sibilia J, Sordet C. An original biotherapy in auto-immune disorders. Rev Med Interne ; Efficacy of B-cell-targeted therapy with Rituximab in patients with rheumatoid arthritis. B-cell depletion in the treatment of patients with systemic lupus erythematosus:

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